t.11 síndromes constitucionales

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    "

    !"#$ &&' ()*)+,$-+.+/0$ 1" .+* *0213+#"* 4+2*-)-54)+2$."*

    #$%&'(

    &6

    789:; (>?;@A6

    ")")

    *+,-+./01./ 23.-3./4)")5)

    67+8.+)

    B6789:; 9>

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    5

    &6 789:; (>?;@A6

    &6&6 !>=C>;H!G;H E+ 2/43. 7+ +4 3.B//> >+ .+:-1+:0/ 0].,72/ D/.J/ >+ 1

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    A

    9/ -].>7>/ >+ 2/43. 3 -"3#W.)*)* :+ .+/47P/ -3. 43: ,]03>3: :7B17++4 +:-/273)

    ` E+21544)W2) (: +4 -/:3 >+4 2/43. >+ 1< 21+.-3 / 30.3 -3. 237.+203)

    ` E+2U"44)W2) b+ >+/ >+ 2/43. -3. 23..7++ /7.+)

    ` >U$,+3$4)W2) \].>7>/ >+ 0+,-+./01./ / 0./D]: >+ 4/ 0./+ 4/ -7+4V:1>3.W ? 4/ .+:-7./27;+ 4/ ,/Y/+ 4/

    0/.>+)

    ` >. *"X+) c3,8.+ ? ,1X+. 07+7@+.++4 27243

    ,+ ,1:214/. 7?;>6

    %+127>3 -3. 2/1:/: /X++4 2+3.

    9/ Z)"V3" + ,)3"X)$ +: 1< /1,++ 4/ 0+,-+./01./ 23.-3./4 R1+ :38.+-/:/ 43:

    F[6\]E "2 .$ 3"/)W2 $X).$3P/23,-/Y/>/ >+ +:0/>3 ,/4+:0/. B+J/S :7+3 ,F: 8/X/ +< L3./: 0+,-./+ 4/

    ,/Y// +< 4/: L3./: >+ 4/ 0/.>+ VE_OOdM_OO -),W) b+ >+

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    E

    *(=\(eQ*feQ Qg&9Qe

    6(he#'f9Q AK d AKSM i'

    6&(he( AKSN d E" i'

    c&\(e\&e(g&Q jE" i'

    E+2*"45"24)$* 1" .$ Z)"V3"'

    9/ @7+8.+ -.3>12+ 1< 7,-3.0/+,//: >+ 3UJB++87>3 @1/,++ 4/ @7+8.+ +: 233 -3.R1+

    32/:73

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    G

    93: *)/2+* N *02-+#$* `5" ,5"1"2 $4+#,$e$3 $ .$ Z)"V3" D/.J/< +< @1+ 4/

    @/:+ >+4 +:0/>3 @+8.74 V@/:+ >+ 7+ .+/X1:0+ >+ 4/ + +:0/>3 3 >+

    ,/+ 47:7: 3 >+ .+03./>S @3.,/ -/.0+ >+ 4/ .+:-1+:0/ >+4 b$' / 4/>+,// >+ 1< .+/X1:0+ >+ 4/ 0+,-+./01./ -3. -/.0+ >+4 2+3.) (< 4/ @/:+ >+ 7+4 -.32+:3 >+ +>7++ @1+.0+: 0+,843.+:)

    ` H5#"2-+ 1" .$ Z3"45"24)$ 4$31)$4$

    ` H5#"2-+ 1" .$ Z3"45"24)$ 3"*,)3$-+3)$

    ` :+.+3"* #5*45.$3"*

    f E"Z$."$

    f E$.+3 N "23+Y"4)#)"2-+ 45-g2"+ V@/:+ >+ 47:7: 3 0+.,7+ /

    ` 751+3$4)W2_ @/:+ >+ 47:7:) Q-/.+2+ 21/3 :+ -37>/ >+ 2/43.)

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    I

    c/? R1+ >7@+.++ 4/ K),"3-"3#)$) (< /,83: 2/:3: :+ -.3>12+ 1+ 4/ *T 23.-3./4 +: >+:23/ "X4"1)"21+ .$

    4$,$4)1$1 1". +3/$2)*#+ ,$3$ ".)#)2$3 ". "X4"*+ 1" 4$.+36

    d (4 0+.,3:0/03 L7-30/4F,723 @J:72/ +U0.+,/S *T /,87++ 2/43.lWS +/> +32.7

    ,+0/8;472/ 7/: VEOi' 3 ,F:W

    m Q-472/27;< :38.+ 4/ :1-+.@727+ 210F+ 23,-.+:/:S 03/44/: +,-/-/>/: >+/B1/ 0787/ V"Md55i'W)

    m h/Y3: 23< /B1/ 0787/ 3 0+,-4/>/)

    m $3 10747P/. 8/Y3: >+ /B1/ @.J/

    ` ="1)1$* Z$3#$4+.W/)4$*' b+ 10747P/< Zg3#$4+* $2-)-L3#)4+* + $2-),)3L-)4+*S R1+

    />+,F: -.3>12+< 1

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    K

    ="4$2)*#+ 1" $44)W2 1" .+* 4+3-)4+)1"* N .+* $2-))2Z.$#$-+3)+* 2+ "*-"3+)1"+*

    ^H@9>M'93: 23.07237>+: 7+ 4/ @3:@347-/:/ Q5 ,7++,3:

    +3: B.1-3:_

    d

    A"*)W2 1)3"4-$ *+V3" $./52+ 1" .+* 4+#,+2"2-"* "*-354-53$."*V,+,8.//Y3 >+4 Q%$ -3. ./>7/273

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    M

    93: 3$1)4$."* .)V3"*:3< ,34]214/: R1+ 23

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    N

    B6B =>EH9@7= H:HC!HE@J9 E>AGAH; h :>(@9@E@J9 :> 9>

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    "O

    f;M'-.3>12+ >+:0.1227;< 432/4S >+:0.1227;< +3: V,+0F:0/:7:W ? 0./:03.

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    ""

    B6F6& EH;HE!>;87!@EH7 :> AH7 9>9@a9H76

    &6 E3"4)#)"2-+ ."2-+V,+:+: 3 /Y3:W) =703:7: +:2/:/:)

    B6 A+4$.)l$1+6 E3"4)#)"2-+ "X,$2*)U+P 2+ )2Z).-3$-)U+)

    F6 !5#+3"* 3"1+21"$1+*P V)"2 1".)#)-$1+* N $ U"4"* "24$,*5.$1+*) $3 :1+4+7D/. 13:I6 EL.5.$* V)"2 1)Z"3"24)$1$*V,/>1./:W) 9/: 2]414/: :3< ,1? -/.+27>/: 3

    -.F2072/,++ +:;@/B3 3 >+

    +:0;,/B3 -1+>+ -.3>127. 1

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    "5

    !=>!D7!H7@7 A@9(Ja>9HV/ 0./D]: >+ DJ/ 473 >+ ,/47B/> >+ 13 >+ +U0++ 4/ + / ? -+3. -.3!@+:/..3443 >+ 1< 01,3. ,/47B7@72/ 4/ +:0.1201./ >+ 4/ 2]414/ 3.7B73 >+ 3.7B+R17.7>/ ? 32/:73/ -3. 4/ /21,14/27;< >+ 4+:73

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    "A

    2/:3: 4/ 4+:7;< /@+20/ /4 Q%$ 2+414/. -+.3 3: 43: 77D7>13: +U-1+:03:S 43

    R1+ 772/ 4/ /> >+ @/203.+: +;B++>3. >+4 "Gq >+ 03>3: 43:

    01,3.+: :3< /0.781784+: / /B++ 4/ L+-/0707:S +02)W /13

    +< 8/20+.7/: V-+X_ @#(&8/-)82#' !A(/'&WS L37/1227;< >+

    /@4/03U713: +U-1+:03: / ./>7/273+

    :1:0/

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    "E

    +)'8%) ,# () )!/!2/*&* 8#(1()' / +1#'2# 8#(1()' !'/:')+),) !)') &+!#,&' ()

    +1(2&!(&8)8&90 ,# () 8J(1() ,)K),) #0 *1 :#0/+)" L# #02,# M1# () &0)82&;)8&90

    / #( ,#6#82/ #0 #*2# >LN 6);/'#.8) () !'/,188&90 ,# 0#/!()*&)*"

    B6[6 i@7! AH7 9>3 /3.S 23,3 /

    >7:0/++

    R1+ :+ 3.7B7+ 4/: 1403:

    >+-++ >+4 07-3 >+ 2F+-+7+3 >+4 07-3 >+

    01,3.) (< +4 2/:3 >+ 43: 3 +:0+ -.32+:3 :+ -.3>12+ 23< ,12L/ ,/?3.

    ./-7>+PS -1>7+3 71./. :;43 1+87>3 / R1+ 4/: 2]414/: R1+23+P R1+ 4/: R1+ 231403S -3. 43

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    "G

    R1+ +4 >+:/..3443 ? +D34127;< >+ 43: 01,3.+: +< 12+< +< 1< -+.73>3 >+

    07+,-3 ,++ 4/: 1./. /Y3:)

    " (H7> @9 7@!G'

    r/ +U7:0+ 13 >+ 3.7B++ >1./. ++ :J+-++. >+ D/.73:

    @/203.+: 23,3 +4 07-3 >+ 2F+ 0+X7>3 +-70+47/4 B4/14/.)n7$34+#$_ 01,3. +< 0+X7>3 23

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    "I

    d =$2)Z"*-$4)+2"* .+4$."*'

    6!"#$%&'()*$+ -.*'()*&"$+ /$" 0%1&*) &-$'#&/)V-)+ 7+ >+:/ >+ B./:/ :18210F

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    "K

    ` H2"#)$ N +-3$* $.-"3$4)+2"* 1" .$* 4L.5.$* *$2/502"$*

    ` A"*)+2"* /.+#"35.$3"* N +V*-3544)W2 ,3+154)1$ ,+3 .+* ,3+154-+* -5#+3$."*P

    B6&S :@Ha9J7!@E< :> AH7 9>7/B+@7+ 2F

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    "M

    f o5)#)+-"3$,)$) 9/ R17,730+./-7/ +: +4 1:3 / + @F.,/23: -/./

    >+:0.17. 4/: 2]414/: 2/+0+/> >+ 2.+2+. ? >7D7>7.:+) (:03:

    @1+.0+: @F.,/23: 4)345.$2"2 ". -+33"2-" *$2/502"+ N 1$e$2 1" Z+3#$ 2+ *"."4-)U$ $

    .$* 4L.5.$* `5" "*-g2 43"4)"21+ "2 Z+3#$ $4-)U$) %+87>3 / R1+ 4/: 2]414/: 2/7D7>+< ,F: .F-7>/,+/Y3 / 4/: 2]414/: + 1< 07+,-3

    D/.7/84+ >+ >+:2/343.

    >7@1:3 3 432/47P/>3

    o G.4"3$4)+2"*:/+-++< >+ 4/ 432/47P/27;< >+4 01,3.S >+ 4/ >3:7: >+ ./>7/27;< />,7/ ? >+ 4/

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    "N

    >1./27;< >+4 0./0/,7+730+./-7/ /@+20/S />+,F: >+4 01,3.S / 4/: 2]414/:

    432/47P/>/: +< +4 F.+/ 0./0/>/) \1+>+S 23,3 4/ R17,730+./-7/S -.3D32/. #54+*)-)* 3

    7+ 4/: ,123:/: >7B+:07D/:) (< -/27++ 2/8+P/ ? 21+443

    -.+:++ B4F14/: :/47D/.+:) \/27+3: / ./>730+./-7/ +< P33,7+< +U-+.7,+3,7+4 +:0/>3 +-++ >+4 B./>3 >+ /B.+:7;< >+ 4/ 27.1BJ/ R1+ / :1 D+P

    +:0F +< @1+ 4/ 7+ 2/8+P/S 21+443S +:;@/B3S +:0;,/B3 ? -F+ /403 .7+:B3 -/./ >+:+++:

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    5O

    23

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    5"

    (U7:0+< >7D+.:3: 07-3: >+ 7+ 4/: 23,7>/:

    ` (D70/. :/83.+: ? 343.+: @1+.0+: >+ 4/ 23,7>/)

    ` (D70/. 0+,-+./01./: +U0.+,/: >+ 43: /47,+/> -.+23P)

    ` b+ >+8+< 03,/. /47,+7C>E8(@EH7)

    C$4)"2-"* 4+2 $.-"3$4)+2"* 1". /5*-+'

    ` (D70/. 0+,-+./01./: +U0.+,/: >+ 43: /47,+

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    55

    C$4)"2-"* 4+2 1)$33"$'

    ` h+8+. /81/3:)

    ` (U2417. 4+2L+ ? >+.7D/>3:)

    ` 97,70/. /47,+

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    5A

    EMHA@=>9!HE@J9 ?D7@EH H:HC!H:H H?HM

    b7 4/ /47,+72733 4/ >++< *5*-)-5)3P + "23)`5"4"3 .+* ,.$-+*L+2L3: )

    b+ 23,+.27/47P/< +< >7:07

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    5E

    :M9G!;@E@J9 H;!@(@E@HA >9!>;HA h CH;>9!>;HA

    '1/3 +4 -/27++21/>/ -3. DJ/ 3./4 :+ -3>.F 10747P/. 1

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    5G

    F 789:; :> @9=G9(@E@>9E@H6

    F6&6 >A 7@7!>=H @9=G9@!H;@+ -.30+227;< 3 >+ 2/-/27>/> >+ .+:7:0+R17+.+ B./27/: / 1< 23+@+/: -3. +4 :7:0+,/ 77:077C>E8(@EH < 9H!G;HA)

    e+-.+:++ 43: 0+X7>3:W_

    @/B3270/< 21+.-3: +U0./Y3:S ? -.+:+

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    5I

    o EL.5.$* 9t ^9$-53$. t).."3M':3< 1< 07-3 >+ 47+:0.1?+ 4/: 2]414/: >+4

    L1]:-+> 7/: -3. ,72.33.B/+ .+-.3>1227;< 7+@++:0.1227;+ 4/: 2]414/: 7/:

    o >. *)*-"#$ 1". 4+#,."#"2-+' (:0F @3.,/>3 -3. 1+ -.30+J+

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    5K

    F6&6B6 @9=G9@:H: H:oG@;@:HP >7C>E8(@EH < H:HC!H!@kH6

    '1/3 4/: >+@+

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    5M

    v.+23.>/.v 1

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    5N

    F6B6 @9=G9@uHE@J9 HE!@kH h CH7@kH' kHEG9HE@J9 h 7G>;;HC@H6

    9/ 7

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    AO

    R1+ -+.,/

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    A"

    F6F6B6AH7 ;>HEE@7 :> i@C>;7>97@?@A@:H:6

    9/ L7-+.:+/> +: 13 +U/B+./>3 3 73 -.3>127+3 7+ .+/2273+ L7-+.:+/>)

    F6F6F6HG!

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    A5

    2703R17

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    AA

    I6789:; =>!H?JA@E+ 1+ :/41> R1+ -1+>+< /-/.+2+. >+

    @3.,/ :7,140F3: -3. 4/ 23,87+

    @/203.+: B++ D7>/ ? R1+ /1,+/>+: >+ >+:/..344/. 2/.>73-/0J/:S /227>+7/8+0+:

    07-3 &&)

    9/ +>/> >+ 43: 77D7>13: -.3-++2+. >+ bJ.3,+ =+0/8;4723 L/ 7>3

    8/X/3 >+ @3.,/ >./,F072/) b7 /+ -/27++ .7+:B3 +:0F :701/>3 +< 03,3 / 43: AG /Y3:S 43 21/4 38+>+2+ / 4/

    0+++:>+ +0/-/: ,1? 0+,-./+ 4/ D7>/S L/27/ 43: ,/43: LF8703: >+/47,++ 4/ -384/27;< +< B++ 43: -/27+ 3 :38.+-+:3 -.+:+7/B+ b= :+ 8/:/ +< 4/ -.+:++ /4 ,++ 43: -.7

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    AE

    `

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